KIDNEY - Adult polycystic disease

The specimen is a transected kidney and includes a short portion of ureter. Multiple small cysts are seen scattered throughout the kidney. These are predominantly situated within the renal cortex, although renal medullary involvement is also identified. The features are those of early adult polycystic kidney.
The patient was an 11 year old female who died of subarachnoid haemorrhage and had bilateral adult polycystic renal disease. There was a family history of polycystic kidney with disease being reported in both the patient's mother and maternal grandmother.