The uterus is very small; the right ovary has been removed entire for histology while the left ovary
is represented by a small nodule below the tip of the tube.
This woman presented at the age of 37 because her hair was beginning to fall out. She
suffered primary amenorrhoea. Laparoscopy showed "streak" ovaries and a small uterus. Her
chromosome pattern was XY. It was decided to remove the ovaries because of the risk of
development of a gonadoblastoma and the uterus was removed as well to facilitate replacement