Description
This shows two portions of skull and one clavicle cut longitudinally. The skull shows haemorrhagic
tumour, both on the outer aspect and on the inner aspect. The tumour is roughly nodular and tumour
tissue is present between the tables. In the clavicle, the tumour is less well defined, but is extending
through much of the length of the bone.
History
This young man presented at the age of 21 with a large pelvic tumour; this was
retroperitoneal and obliterated the pelvic cavity displacing the left ureter and sigmoid colon. The
tumour did not appear to be encapsulated, and numerous abnormal nerves were related to it.
Removal was incomplete. The history was that of a partially differentiated ganglioneuroma. He
continued to have pelvic pain; he developed intermittent haematuria and ultimately an aplastic
anaemia and hyperglycaemia (? secondary to steriods). He required many transfusions, which he
ultimately declined. At autopsy, five years after diagnosis, he showed a haemorrhagic tumour mass
in the pelvis with obstruction of the left ureter; secondary deposits in liver, ribs, vertebral bodies,
clavicles and skull and lung.